Radiol Clin North Am 1993 May;31(3):617-630
Cystic fibrosis. Clinical update for radiologists.
Orenstein DM, Bowen A
The clinical features and current management of cystic fibrosis are reviewed, with emphasis on pulmonary manifestations. Pulmonary radiographic findings in cystic fibrosis are illustrated. The role of transplantation as a therapeutic avenue is discussed. Recent discoveries--the specific genetic mutation in cystic fibrosis, the elucidation of the cellular defect, and the development of gene-transfer techniques to correct the cellular defect in vitro--have generated fresh excitement in the search for an ultimate cure for cystic fibrosis.
PMID: 8497594, MUID: 93268867
